Multiple skipped craniospinal arteriovenous malformations complicated with hydrocephalus and syringomyelia

Arteriovenous malformations (AVMs) can occur within the intracranial or spinal region. When AVMs occur within the central nervous system, they are usually solitary. Central nervous system AVMs are known to be more common within the intracranial compartment when compared with the spinal region. AVMs within the intracranial compartment can be complicated with hydrocephalus, whereas AVM within the spinal cord may be associated with syringomyelia, just like a posterior fossa AVM. The co-existence of cranial and spinal AVMs has only been reported in very few cases in the literature. We report a case of multiple and skipped cerebral and juvenile spinal AVM associated with hydrocephalus and cervicothoracic syringomyelia in a 26-year-old female.