Congenital long QT syndrome and patent ductus arteriosus: A rare surgical scenario

Congenital long QT syndrome (LQTS) is a rare cardiac condition characterized by abnormality of either sodium or potassium ion channels resulting in prolongation of QT interval and thereby predisposing to life-threatening arrhythmia. Once the syndrome is diagnosed, measures should be taken to avoid s...

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Veröffentlicht in:Annals of pediatric cardiology 2021-01, Vol.14 (1), p.85-87
Hauptverfasser: Raja, Javid, Menon, Sabarinath, Venkata, Devarakonda, Unnikrishnan, K, Namboodiri, Narayanan
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Sprache:eng
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Zusammenfassung:Congenital long QT syndrome (LQTS) is a rare cardiac condition characterized by abnormality of either sodium or potassium ion channels resulting in prolongation of QT interval and thereby predisposing to life-threatening arrhythmia. Once the syndrome is diagnosed, measures should be taken to avoid sudden cardiac death. We present a rare case of LQTS associated with patent ductus arteriosus in a child, and a unique approach was used in managing both conditions.
ISSN:0974-2069
0974-5149
DOI:10.4103/apc.APC_146_19