Primary appendiceal Burkitt's lymphoma presenting as acute appendicitis: An extremely rare case report and review of the literatture

Primary lymphomas of appendix are extremely rare tumors. The incidence is 0.015% out of all gastrointestinal lymphomas; furthermore, limited data is available in literature. The appendiceal neoplasms are most commonly presented as acute appendicitis followed intestinal obstruction, intussusception or perforation. We present a case of a 22 year-old male patient who presented with acute appenditis and underwent emergency laparotomy. On abdominal exploration, swollen and enlarged appendix measured 3cm was present for which appendectomy were performed. The histopathological examination of appendectomy specimen revealed a Burkitt's Lymphoma. The patient received R-COPADEM protocol of chemotherapy. Primary gastrointestinal lymphoma is a extremely rare neoplasm without guidelines for therapy. •Burkitt lymphoma is an aggressive non-hodgkin b-cell lymphoma.•The occurrence of primary Burkitt's lymphoma of appendix is extremely rare.•The appendiceal neoplasms are most commonly presented as acute appendicitis.•The diagnosis of kimura disease is confirmed by surgical biopsy.•The diagnostic of Burkitt's lymphoma was only made after histopathological examination, so should be done.•The surgery and chemotheray constitue a best traitement for burkitt's lymphoma of appendix presenting as acute appendicitis.