Pulmonary extraskeletal myxoid chondrosarcoma: A case report and literature review

Highlights • Extraskeletal myxoid chondrosarcoma (EMC) is a rare tumor characterized by the multinodular growth of primitive chondroid cells in an abundant myxoid matrix. • EMC is categorized as a tumor of uncertain differentiation by the 2002 WHO classification. • EMC has shown to have the recurrent balanced chromosomal translocation t(9;22) (q22;q12.2), which leads to the oncogenic fusion gene EWSR1-NR4A3. • EMC usually presents in male patients beyond their fifth decade as a slow growing, palpable mass in the extremities. • Pulmonary extraskeletal myxoid chondrosarcomas are extremely rare with only isolated case reports found in the literature.