Two-stage release in Streeter's dysplasia

Streeter's dysplasia is a rare disorder of congenital constricting bands, occurring in 1–10 000 birth, with no sex predilection. In severe cases, it is associated with autoamputation of distal extremities such as fingers and toes. Recent advances have made it possible, in developed countries, t...

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Veröffentlicht in:BMJ case reports 2015-04, Vol.2015, p.bcr2014207568
Hauptverfasser: Naqvi, Zohaib Gulzar, Rao, Irfan, Anwer, Wahid, Yaseen, Tahir
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Sprache:eng
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Zusammenfassung:Streeter's dysplasia is a rare disorder of congenital constricting bands, occurring in 1–10 000 birth, with no sex predilection. In severe cases, it is associated with autoamputation of distal extremities such as fingers and toes. Recent advances have made it possible, in developed countries, to recognise this condition in the prenatal period and to initiate prompt intrauterine management, however, these, being uncommon procedures, need technical advances and experienced hands. In developing countries, recognition of the condition with timely management of primary and associated abnormalities required. We present a case of a 4-month-old child with type IV Streeter's dysplasia associated with right flexible clubfoot, who underwent successful two-stage release of symptomatic constricting bands from bilateral legs.
ISSN:1757-790X
1757-790X
DOI:10.1136/bcr-2014-207568