Central Nervous System Involvement in Congenital Visceral Fibromatosis

Congenital visceral myofibromatosis is an uncommon disorder characterized by multiple tumors of myofibroblastic origin in the neonatal period. The natural history of the disorder has been well delineated. The myofibro blast is the cell of origin of the tumor. This is a report of a patient in whom mu...

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Veröffentlicht in:	Fetal and pediatric pathology 1985, Vol.3 (2-4), p.329-340
Hauptverfasser:	Adickes, Edward D., Goodrich, Paul, Auchmoedy, Joseph, Bickers, Gayle, Bowden, Bruce, Koh, Jack, Nelson, Robert M., Shuman, Robert M., Wilson, Richard B.
Format:	Artikel
Sprache:	eng
Schlagworte:	Adult Brain Neoplasms - congenital Brain Neoplasms - pathology Brain Neoplasms - ultrastructure central nervous system congenital visceral fibromatosis Female Fibroma - congenital Fibroma - pathology Fibroma - ultrastructure Humans Infant, Newborn Male Microscopy, Electron Neoplasms, Multiple Primary - congenital Neoplasms, Multiple Primary - pathology Neoplasms, Multiple Primary - ultrastructure Pregnancy Spinal Cord Neoplasms - congenital Spinal Cord Neoplasms - pathology Spinal Cord Neoplasms - ultrastructure
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Zusammenfassung:	Congenital visceral myofibromatosis is an uncommon disorder characterized by multiple tumors of myofibroblastic origin in the neonatal period. The natural history of the disorder has been well delineated. The myofibro blast is the cell of origin of the tumor. This is a report of a patient in whom multiple mesenchymal tumors occurred in the CNS as well as in other organs. Light and electron microiscopic findings of the CNS lesions are similar to those of the somites and viscera.
ISSN:	1551-3815 0277-0938 1551-3823
DOI:	10.3109/15513818509078793