Totally anomalous pulmonary venous connection with intact atrial septum

Background Total anomalous pulmonary venous connection with intact interatrial septum is extremely rare. Aims In these patients, a right to left shunt through a ventricular septal defect or a patent ductus arteriosus is mandatory to maintain the systemic circulation. Mechanical or physiological restriction of shunting through these pathways results in rapid clinical deterioration. Discussion We describe the anatomical findings with surgical repair in one such 10‐day‐old baby.