Nonteratoid Medulloepithelioma Presenting in a 78-Year-Old Male

Background: Medulloepithelioma is a rare congenital neoplasm derived from precursors of the nonpigmented ciliary epithelium of the ciliary body. The average patient age at clinical presentation is 3.8 years. Case Presentation: We present the case of a 78-year-old male with progressive lens subluxati...

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Veröffentlicht in:Ocular oncology and pathology 2016-10, Vol.2 (4), p.218-221
Hauptverfasser: Burris, Christopher K.H., Papastefanou, Vasilios P., Thaung, Caroline, Hay, Gordon, Grantham, Marianne, Cohen, Victoria M.L.
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Sprache:eng
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Zusammenfassung:Background: Medulloepithelioma is a rare congenital neoplasm derived from precursors of the nonpigmented ciliary epithelium of the ciliary body. The average patient age at clinical presentation is 3.8 years. Case Presentation: We present the case of a 78-year-old male with progressive lens subluxation and ocular hypertension who was found to have a ciliary body mass. After enucleation for presumed ciliary body melanoma, histopathology showed a nonteratoid medulloepithelioma. Cytogenetic analysis revealed abnormalities in chromosomes 3 and 8. Conclusion: Medulloepithelioma is often initially misdiagnosed. Though congenital in nature, it can exhibit rapid growth, have chromosomal abnormalities, and must be considered in all age groups.
ISSN:2296-4681
2296-4657
DOI:10.1159/000445209