Propriospinal myoclonus associated with gluten sensitivity in a young woman

Abstract Propriospinal myoclonus (PSM) is a rare movement disorder characterized by involuntary axial jerks originating from muscles innervated by multiple spinal segments. Most cases of PSM are idiopathic. Gluten sensitivity is a multisystemic autoimmune condition which may be associated with various neurological disorders, most commonly peripheral neuropathy and cerebellar ataxia. We report a case of a young woman who developed PSM in the setting of gluten sensitivity, indicating that gluten sensitivity should be considered in the differential diagnosis of PSM such that a gluten challenge test may prove diagnostically useful.