Cushing syndrome due to ectopic adrenocorticotropic hormone secretion in a 3-year-old child

Ectopic adrenocorticotrophic hormone (ACTH) secretion is a rare cause of Cushing syndrome in paediatric age, due to tumours arising from different tissues. To date, only 11 reports of ACTH-secreting pancreatic tumours in children and adolescents exist in the literature. We present a paediatric case...

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Veröffentlicht in:	Journal of Pediatric Endocrinology and Metabolism 2011-04, Vol.24 (3-4), p.219-222
Hauptverfasser:	Matarazzo, Patrizia, Tuli, Gerdi, Tessaris, Daniele, Verna, Francesca, Rabbone, Ivana, Lezo, Antonella, Brunati, Andrea, Salizzoni, Mauro, Carbonaro, Giulia, Terzolo, Massimo, Reimondo, Giuseppe, Papotti, Mauro, Lala, Roberto
Format:	Artikel
Sprache:	eng
Schlagworte:	Adrenocorticotropic Hormone - metabolism Carcinoma, Acinar Cell - complications Carcinoma, Acinar Cell - metabolism Carcinoma, Acinar Cell - pathology Child, Preschool children Combined Modality Therapy Cushing syndrome Cushing Syndrome - etiology Cushing Syndrome - metabolism Cushing Syndrome - pathology Digestive System Surgical Procedures ectopic ACTH secretion Female Humans Ketoconazole - therapeutic use pancreas acinar cell tumour Pancreatic Neoplasms - complications Pancreatic Neoplasms - metabolism Pancreatic Neoplasms - pathology Treatment Outcome
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Zusammenfassung:	Ectopic adrenocorticotrophic hormone (ACTH) secretion is a rare cause of Cushing syndrome in paediatric age, due to tumours arising from different tissues. To date, only 11 reports of ACTH-secreting pancreatic tumours in children and adolescents exist in the literature. We present a paediatric case of Cushing syndrome caused by ectopic ACTH secretion. This was caused by a large acinar cell carcinoma that developed in the pancreas of a 3-year-old girl.
ISSN:	0334-018X 2191-0251
DOI:	10.1515/jpem.2011.100