Chronic catastrophic-like antiphospholipid syndrome: a “smoldering” variant?

Catastrophic antiphospholipid syndrome (CAPS) is characterized by life-threatening diffuse thrombotic manifestations involving particularly small vessels of kidney, lungs, brain and skin. We report a 20-year-old female with systemic lupus erythematosus and secondary antiphospholipid syndrome who pre...

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Veröffentlicht in:	Rheumatology international 2009-11, Vol.30 (1), p.123-125
Hauptverfasser:	Athanazio, Daniel, Rocha, Maria Cristina, de Souza e Souza, Túlio Geraldo, e Silva, Natália Oliveira, Jezler, Sérgio, Santiago, Mittermayer Barreto
Format:	Artikel
Sprache:	eng
Schlagworte:	Antiphospholipid Syndrome - classification Antiphospholipid Syndrome - diagnosis Antiphospholipid Syndrome - drug therapy Antiphospholipid Syndrome - immunology Autoimmune diseases Case Report Catastrophic Illness Chronic Disease Drug Therapy, Combination Female Humans Immunosuppressive Agents - therapeutic use Lupus Erythematosus, Systemic - complications Lupus Erythematosus, Systemic - drug therapy Lupus Erythematosus, Systemic - immunology Medical diagnosis Medicine Medicine & Public Health Rheumatology Tomography, X-Ray Computed Treatment Outcome Young Adult
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Zusammenfassung:	Catastrophic antiphospholipid syndrome (CAPS) is characterized by life-threatening diffuse thrombotic manifestations involving particularly small vessels of kidney, lungs, brain and skin. We report a 20-year-old female with systemic lupus erythematosus and secondary antiphospholipid syndrome who presented typical organ and histological involvement as seen in CAPS but with protracted course suggesting a “smoldering” form of the disease.
ISSN:	0172-8172 1437-160X
DOI:	10.1007/s00296-009-0913-8