Congenital stenosis of pulmonary veins at their atrial junctions

1. 1. A case of congenital stenosis of the pulmonary veins is presented. 2. 2. The brief literature on congenital pulmonary venous stenosis is reviewed. Only one similar case was found. Two other reported cases of congenital stenosis were complicated by cardiac anomalies and presented different types of stenosing lesions. 3. 3. The anatomy of this lesion with special reference to the possibility of surgical correction is discussed. 4. 4. The secondary effects of pulmonary venous obstruction in this case are: pulmonary hypertension, hyperemia, edema, focal fibrosis, hemosiderosis, an unusual response to inflammation, and some shunting of pulmonary venous blood to the systemic return.