Infradiaphragmatic total anomalous pulmonary venous connection

A study of 4 cases of uncomplicated total anomalous pulmonary venous drainage, in which the connection with the systemic circuit is in the region of the porta hepatis, revealed similar clinical and radiologic findings, so that in the fourth case the diagnosis was suspected and confirmed by angiocardiographic study. Mainly due to the obstruction of pulmonary venous outflow, this form of total anomalous pulmonary venous drainage forms a distinct entity and the physiologic disturbance is quite different from those anomalies of the venous return in which the connection with the systemic circulation is above the diaphragm.