Anomalous origin of the right coronary artery from the main pulmonary artery

An adolescent boy with anomalous origin of the right coronary artery from the main pulmonary artery is presented. Although he had been asymptomatic, a to and fro heart murmur and slight cardiac enlargement suggested a cardiac malformation. Once the diagnosis was established by cardiac catheterization and angiocardiography, the defect was corrected by transplanting the anomalous coronary vessel to the aorta. This is the first pediatric patient with isolated anomalous right coronary artery from the main pulmonary artery whose condition was diagnosed ante mortem and the first patient to have surgical correction of the malformation.