Ameloblastoma associated with basal cell nevus (Gorlin) syndrome: CT findings

Multiple jaw cysts are a characteristic manifestation of basal cell nevus (Gorlin) syndrome. In contrast to the frequent odontogenic keratocysts, ameloblastoma only rarely occurs in the jaw. Computed tomography is essential to delineate the extent of these radioresistant lesions, which must undergo marginal resection. We present such a case, not only to stress the importance of CT evaluation but also to briefly review the unusual association of ameloblastoma with Gorlin syndrome.