Cold bone scans as a sign of hemorrhagic infarcts of the spine in Gaucher's disease

The most common form of Gaucher's disease, type 1 (chronic non-neuronopathic), results in accumulation of glucocerebroside in reticuloendothelial cells of the spleen, liver and bone marrow, with frequent occurrence of bone pain due to vaso-occlusive crisis. We report the finding of a "cold...

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Veröffentlicht in:Pediatric radiology 1997-06, Vol.27 (6), p.514-516
Hauptverfasser: DOLEN, E. G, BERDON, W. E, RUZAL-SHAPIRO, C
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Sprache:eng
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Zusammenfassung:The most common form of Gaucher's disease, type 1 (chronic non-neuronopathic), results in accumulation of glucocerebroside in reticuloendothelial cells of the spleen, liver and bone marrow, with frequent occurrence of bone pain due to vaso-occlusive crisis. We report the finding of a "cold" vertebral body on bone scan in two patients with Gaucher's disease and bone crisis. Photopenia was so striking as to give the appearance of a "missing" vertebra. Concurrent plain films appeared normal. In one patient Gaucher's disease had not previously been diagnosed.
ISSN:0301-0449
1432-1998
DOI:10.1007/s002470050170