Malignant Schwannoma located in the retroauricular region

There have been no reports about malignant Schwannoma located retroauricularly in the medical literature we reviewed. Malignant Schwannoma is a very malignant tumor, which is rare. For diagnosis, microscopic and immunohistochemical studies are needed. It is often seen together with neurofibromatosis. The prognosis is very poor and the only available treatment is surgical excision. Although it is known that both radiotherapy and chemotherapy are not effective, we achieved good outcome with this combination applied postoperatively.