A Case Report of Kleeblattschadel (Clover Leaf Skull) Syndrome and it's Dental Findings

A report was made of a 3 year and 9 month old girl with the Kleeblattschadel (clover leaf skull) syndrome. She had a grotesque trilobed skull with bulging at the frontal and temporal parts of the cranium. It was caused by synostosis of the posterior part of the saggital suture; lambdoid suture and coronal suture, and hydrocephaly. Furthermore, exophthalmos, downward displaced ears, deeply recessed nasal root and shortening of the extremities were present. In addition to these general findings, this case also disclosed the following dental findings: 1) Roentgencephalometric analysis revealed hypoplasia of the maxilla and the body of mandibula, and relative mandibula prognathism. 2) Hypoplasia of the maxilla led to such severe cross bite that the upper and lower incisors could not bite against each other. Hypoplasia of the max i l la and mandibula led to shortening of the width and length of both the upper and lower dental arches. 3) The palate had a marked median furrow. 4) Eruption of the upper second primary molars was delayed for a short period.