Sole pulmonary involvement by Langerhans' cell histiocytosis in a child

The case of a boy aged 4 yrs and 7 months, with isolated pulmonary involvement by Langerhans' cell histiocytosis is reported. The presentation of the disease was a sudden pneumothorax, with no previous signs of respiratory disease. The case was confirmed by S-100 and MT1 antibody staining, and...

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Veröffentlicht in:	The European respiratory journal 1993-09, Vol.6 (8), p.1226-1228
Hauptverfasser:	Chatkin, JM, Bastos, JC, Stein, RT, Gaiger, AM
Format:	Artikel
Sprache:	eng
Schlagworte:	Biological and medical sciences Child, Preschool Hematologic and hematopoietic diseases Histiocytosis, Langerhans-Cell - complications Histiocytosis, Langerhans-Cell - diagnosis Histiocytosis, Langerhans-Cell - pathology Humans Lung - diagnostic imaging Lung - pathology Lung Diseases - complications Lung Diseases - diagnosis Lung Diseases - pathology Male Medical sciences Other diseases. Hematologic involvement in other diseases Pneumothorax - etiology Radiography
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Beschreibung
Zusammenfassung:	The case of a boy aged 4 yrs and 7 months, with isolated pulmonary involvement by Langerhans' cell histiocytosis is reported. The presentation of the disease was a sudden pneumothorax, with no previous signs of respiratory disease. The case was confirmed by S-100 and MT1 antibody staining, and was treated with pulse steroids and several pleural drainages, until the boy died after a large bilateral pneumothorax.
ISSN:	0903-1936 1399-3003
DOI:	10.1183/09031936.93.06081226