Single ventricle with truncus arteriosus in siblings

Single ventricle with truncus arteriosus in siblings

Single ventricle and truncus arteriosus (TA) are relatively uncommon congenital cardiac defects. Keith et al. 1.2 reported these lesions to occur, respectively, in 1.1% and 0.4% of children with congenital cardiac defects. The occurrence of TA with a single left ventricle (LV) often has been theoriz...

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Veröffentlicht in:The American heart journal 1981-09, Vol.102 (3), p.456-459
Hauptverfasser: Shapiro, Stephen R., Ruckman, Roger N., Kapur, Sudesh, Chandra, Roma, Galioto, Frank M., Perry, Lowell W., Scott, Lewis P.
Format: Artikel
Sprache:eng
Schlagworte:
Adult
Cardiac Catheterization
Cardiomegaly - complications
Cyanosis - complications
Cyanosis - etiology
Electrocardiography
Female
Heart Rate
Heart Ventricles - abnormalities
Humans
Infant
Male
Pulmonary Valve Stenosis - complications
Truncus Arteriosus, Persistent - genetics
Truncus Arteriosus, Persistent - mortality
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Zusammenfassung:Single ventricle and truncus arteriosus (TA) are relatively uncommon congenital cardiac defects. Keith et al. 1.2 reported these lesions to occur, respectively, in 1.1% and 0.4% of children with congenital cardiac defects. The occurrence of TA with a single left ventricle (LV) often has been theorized as a developmental stage but not previously described. This report describes siblings with the unique association of single LV with rudimentary right ventricular (RV) outflow chamber, TA type I, ostium primum atrial septal defect (ASD), and common atrioventricular (AV) valve.
ISSN:0002-8703
1097-6744
DOI:10.1016/0002-8703(81)90322-7