Chylothorax complicating Gorham’s disease

Gorham’s disease is a rare disorder characterized by a proliferation of thin-walled lymphatic vessels (lymphangiectasia) resulting in an osteolysis. A chylothorax is present in about one-fifth of the patients and carries a poor prognosis. In this circumstance, surgery including thoracic duct ligatio...

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Veröffentlicht in:The Annals of thoracic surgery 2001-09, Vol.72 (3), p.937-939
Hauptverfasser: Chavanis, Nicolas, Chaffanjon, Philippe, Frey, Gil, Vottero, Gabrielle, Brichon, Pierre-Yves
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Sprache:eng
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Zusammenfassung:Gorham’s disease is a rare disorder characterized by a proliferation of thin-walled lymphatic vessels (lymphangiectasia) resulting in an osteolysis. A chylothorax is present in about one-fifth of the patients and carries a poor prognosis. In this circumstance, surgery including thoracic duct ligation, pleurodesis, and excision of involved tissue is probably the treatment of choice. It is facilitated by a precise radiological assessment using a computed tomographic scanning coupled with a lymphography. We report such a case.
ISSN:0003-4975
1552-6259
DOI:10.1016/S0003-4975(00)02417-6