Anaesthesia for liver transplantation in a patient with methylmalonic acidaemia

Summary Liver transplantation is an accepted modality of treatment in some patients with inborn errors of metabolism. We present a child with methylmalonic acidaemia who had successful liver transplantation. The pathophysiology, medical and anaesthetic managements are discussed.

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Bibliographische Detailangaben
Veröffentlicht in:	Pediatric anesthesia 2000, Vol.10 (2), p.215-218
Hauptverfasser:	Ho, David, Harrison, Victor, Street, Neil
Format:	Artikel
Sprache:	eng
Schlagworte:	Abdominal surgery. Urology. Gynecology. Obstetrics Acid-Base Equilibrium - physiology Anesthesia Anesthesia depending on type of surgery Anesthesia, Inhalation Anesthesia. Intensive care medicine. Transfusions. Cell therapy and gene therapy Anesthetics, Inhalation - administration & dosage Biological and medical sciences Humans inborn error of metabolism Infant Isoflurane - administration & dosage Liver Transplantation Male Medical sciences Metabolism, Inborn Errors - surgery Metabolism, Inborn Errors - therapy methylmalonic acid Methylmalonic Acid - blood Preanesthetic Medication Renal Dialysis
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Beschreibung
Zusammenfassung:	Summary Liver transplantation is an accepted modality of treatment in some patients with inborn errors of metabolism. We present a child with methylmalonic acidaemia who had successful liver transplantation. The pathophysiology, medical and anaesthetic managements are discussed.
ISSN:	1155-5645 1460-9592
DOI:	10.1046/j.1460-9592.2000.00451.x