Liver transplantation in children with glycogen storage disease: Controversies and evaluation of the risk/benefit of this procedure

: GSD‐I, III, and IV are congenital disorders of glycogen metabolism that are commonly associated with severe liver disease. Liver transplantation has been proposed as a therapy for these disorders. While liver transplantation corrects the primary hepatic enzyme defect, the extrahepatic manifestations of GSD often complicate post‐transplantation management. Upon review of the English‐language literature, 42 children