One-Step Surgical Approach of a Thoracic Aortic Aneurysm in Wiskott-Aldrich Syndrome
Wiskott-Aldrich syndrome is a primary immunodeficiency characterized by infections, thrombocytopenia, and eczema. We present a 33-year-old man with this syndrome who underwent a one-stage ascending aorta, aortic arch and descending aortic aneurysm repair under moderate hypothermia and continuous vis...
Gespeichert in:
| Veröffentlicht in: | The Annals of thoracic surgery 2007-04, Vol.83 (4), p.1537-1538 |
|---|---|
| Hauptverfasser: | , , , , , , |
| Format: | Artikel |
| Sprache: | eng |
| Schlagworte: | |
| Online-Zugang: | Volltext |
| Tags: |
Tag hinzufügen
Keine Tags, Fügen Sie den ersten Tag hinzu!
|
| container_end_page | 1538 |
|---|---|
| container_issue | 4 |
| container_start_page | 1537 |
| container_title | The Annals of thoracic surgery |
| container_volume | 83 |
| creator | Bernabeu, Eduardo, MD Josa, Miguel, MD Nomdedeu, Benet, MD, PhD Ramírez, José, MD, PhD García-Valentín, Antonio, MD Mestres, Carlos A., MD, PhD Mulet, Jaime, MD, PhD |
| description | Wiskott-Aldrich syndrome is a primary immunodeficiency characterized by infections, thrombocytopenia, and eczema. We present a 33-year-old man with this syndrome who underwent a one-stage ascending aorta, aortic arch and descending aortic aneurysm repair under moderate hypothermia and continuous visceral and cerebral perfusion. Histologic examination showed the presence of an aortitis with granulomatous inflammatory response and multinucleated cells. |
| doi_str_mv | 10.1016/j.athoracsur.2006.10.005 |
| format | Article |
| fullrecord | <record><control><sourceid>proquest_cross</sourceid><recordid>TN_cdi_proquest_miscellaneous_70307418</recordid><sourceformat>XML</sourceformat><sourcesystem>PC</sourcesystem><els_id>S000349750601931X</els_id><sourcerecordid>70307418</sourcerecordid><originalsourceid>FETCH-LOGICAL-c493t-3533e7f5fc116b83438c10fab6c7a01f044b81fc8a55f740eb85c4dd2904287c3</originalsourceid><addsrcrecordid>eNqNksGO0zAQhi0EYrsLr4BygVvKOLYT54JUVsAirbSHFsHNcpwx625iFztB6tvj0EqVOHEa2fPPzK9vhpCCwpoCrd_v13p6DFGbNMd1BVDn7zWAeEZWVIiqrCvRPicrAGAlbxtxRa5T2udnldMvyRVtmGRMworsHjyW2wkPxXaOP53RQ7E5HGLQ5rEIttDF7u8cZ4pNiNMSPM7xmMbC-eK7S09hmsrN0EeXC7ZH38cw4ivywuoh4etzvCHfPn_a3d6V9w9fvt5u7kvDWzaVTDCGjRXWUFp3knEmDQWru9o0GqgFzjtJrZFaCNtwwE4Kw_u-aoFXsjHshrw79c2Gf82YJjW6ZHAYtMcwJ9UAg4ZTmYXyJDQxpBTRqkN0o45HRUEtRNVeXYiqheiSyURz6ZvzjLkbsb8UnhFmwduzQKeMz0btjUsXnayZrPni4eNJh5nIb4dRJePQG-xdRDOpPrj_cfPhnyZmcH5Z2xMeMe3DHH0mrqhKlQK1XS5gOQCogbaM_mB_AK1orgA</addsrcrecordid><sourcetype>Aggregation Database</sourcetype><iscdi>true</iscdi><recordtype>article</recordtype><pqid>70307418</pqid></control><display><type>article</type><title>One-Step Surgical Approach of a Thoracic Aortic Aneurysm in Wiskott-Aldrich Syndrome</title><source>MEDLINE</source><source>Elektronische Zeitschriftenbibliothek - Frei zugängliche E-Journals</source><source>Alma/SFX Local Collection</source><creator>Bernabeu, Eduardo, MD ; Josa, Miguel, MD ; Nomdedeu, Benet, MD, PhD ; Ramírez, José, MD, PhD ; García-Valentín, Antonio, MD ; Mestres, Carlos A., MD, PhD ; Mulet, Jaime, MD, PhD</creator><creatorcontrib>Bernabeu, Eduardo, MD ; Josa, Miguel, MD ; Nomdedeu, Benet, MD, PhD ; Ramírez, José, MD, PhD ; García-Valentín, Antonio, MD ; Mestres, Carlos A., MD, PhD ; Mulet, Jaime, MD, PhD</creatorcontrib><description>Wiskott-Aldrich syndrome is a primary immunodeficiency characterized by infections, thrombocytopenia, and eczema. We present a 33-year-old man with this syndrome who underwent a one-stage ascending aorta, aortic arch and descending aortic aneurysm repair under moderate hypothermia and continuous visceral and cerebral perfusion. Histologic examination showed the presence of an aortitis with granulomatous inflammatory response and multinucleated cells.</description><identifier>ISSN: 0003-4975</identifier><identifier>EISSN: 1552-6259</identifier><identifier>DOI: 10.1016/j.athoracsur.2006.10.005</identifier><identifier>PMID: 17383380</identifier><identifier>CODEN: ATHSAK</identifier><language>eng</language><publisher>New York, NY: Elsevier Inc</publisher><subject>Adult ; Angiography ; Aortic Aneurysm, Thoracic - diagnostic imaging ; Aortic Aneurysm, Thoracic - etiology ; Aortic Aneurysm, Thoracic - surgery ; Biological and medical sciences ; Blood Vessel Prosthesis ; Blood Vessel Prosthesis Implantation - methods ; Brain Ischemia - prevention & control ; Cardiopulmonary Bypass ; Cardiothoracic Surgery ; Follow-Up Studies ; Hematologic and hematopoietic diseases ; Humans ; Immunodeficiencies ; Immunodeficiencies. Immunoglobulinopathies ; Immunopathology ; Male ; Medical sciences ; Perfusion - methods ; Platelet diseases and coagulopathies ; Radiography, Thoracic ; Risk Assessment ; Severity of Illness Index ; Surgery ; Surgery (general aspects). Transplantations, organ and tissue grafts. Graft diseases ; Surgery of the heart ; Surgery of the respiratory system ; Tomography, X-Ray Computed ; Treatment Outcome ; Wiskott-Aldrich Syndrome - complications ; Wiskott-Aldrich Syndrome - diagnosis</subject><ispartof>The Annals of thoracic surgery, 2007-04, Vol.83 (4), p.1537-1538</ispartof><rights>The Society of Thoracic Surgeons</rights><rights>2007 The Society of Thoracic Surgeons</rights><rights>2007 INIST-CNRS</rights><lds50>peer_reviewed</lds50><woscitedreferencessubscribed>false</woscitedreferencessubscribed><citedby>FETCH-LOGICAL-c493t-3533e7f5fc116b83438c10fab6c7a01f044b81fc8a55f740eb85c4dd2904287c3</citedby><cites>FETCH-LOGICAL-c493t-3533e7f5fc116b83438c10fab6c7a01f044b81fc8a55f740eb85c4dd2904287c3</cites></display><links><openurl>$$Topenurl_article</openurl><openurlfulltext>$$Topenurlfull_article</openurlfulltext><thumbnail>$$Tsyndetics_thumb_exl</thumbnail><link.rule.ids>314,776,780,27901,27902</link.rule.ids><backlink>$$Uhttp://pascal-francis.inist.fr/vibad/index.php?action=getRecordDetail&idt=18638648$$DView record in Pascal Francis$$Hfree_for_read</backlink><backlink>$$Uhttps://www.ncbi.nlm.nih.gov/pubmed/17383380$$D View this record in MEDLINE/PubMed$$Hfree_for_read</backlink></links><search><creatorcontrib>Bernabeu, Eduardo, MD</creatorcontrib><creatorcontrib>Josa, Miguel, MD</creatorcontrib><creatorcontrib>Nomdedeu, Benet, MD, PhD</creatorcontrib><creatorcontrib>Ramírez, José, MD, PhD</creatorcontrib><creatorcontrib>García-Valentín, Antonio, MD</creatorcontrib><creatorcontrib>Mestres, Carlos A., MD, PhD</creatorcontrib><creatorcontrib>Mulet, Jaime, MD, PhD</creatorcontrib><title>One-Step Surgical Approach of a Thoracic Aortic Aneurysm in Wiskott-Aldrich Syndrome</title><title>The Annals of thoracic surgery</title><addtitle>Ann Thorac Surg</addtitle><description>Wiskott-Aldrich syndrome is a primary immunodeficiency characterized by infections, thrombocytopenia, and eczema. We present a 33-year-old man with this syndrome who underwent a one-stage ascending aorta, aortic arch and descending aortic aneurysm repair under moderate hypothermia and continuous visceral and cerebral perfusion. Histologic examination showed the presence of an aortitis with granulomatous inflammatory response and multinucleated cells.</description><subject>Adult</subject><subject>Angiography</subject><subject>Aortic Aneurysm, Thoracic - diagnostic imaging</subject><subject>Aortic Aneurysm, Thoracic - etiology</subject><subject>Aortic Aneurysm, Thoracic - surgery</subject><subject>Biological and medical sciences</subject><subject>Blood Vessel Prosthesis</subject><subject>Blood Vessel Prosthesis Implantation - methods</subject><subject>Brain Ischemia - prevention & control</subject><subject>Cardiopulmonary Bypass</subject><subject>Cardiothoracic Surgery</subject><subject>Follow-Up Studies</subject><subject>Hematologic and hematopoietic diseases</subject><subject>Humans</subject><subject>Immunodeficiencies</subject><subject>Immunodeficiencies. Immunoglobulinopathies</subject><subject>Immunopathology</subject><subject>Male</subject><subject>Medical sciences</subject><subject>Perfusion - methods</subject><subject>Platelet diseases and coagulopathies</subject><subject>Radiography, Thoracic</subject><subject>Risk Assessment</subject><subject>Severity of Illness Index</subject><subject>Surgery</subject><subject>Surgery (general aspects). Transplantations, organ and tissue grafts. Graft diseases</subject><subject>Surgery of the heart</subject><subject>Surgery of the respiratory system</subject><subject>Tomography, X-Ray Computed</subject><subject>Treatment Outcome</subject><subject>Wiskott-Aldrich Syndrome - complications</subject><subject>Wiskott-Aldrich Syndrome - diagnosis</subject><issn>0003-4975</issn><issn>1552-6259</issn><fulltext>true</fulltext><rsrctype>article</rsrctype><creationdate>2007</creationdate><recordtype>article</recordtype><sourceid>EIF</sourceid><recordid>eNqNksGO0zAQhi0EYrsLr4BygVvKOLYT54JUVsAirbSHFsHNcpwx625iFztB6tvj0EqVOHEa2fPPzK9vhpCCwpoCrd_v13p6DFGbNMd1BVDn7zWAeEZWVIiqrCvRPicrAGAlbxtxRa5T2udnldMvyRVtmGRMworsHjyW2wkPxXaOP53RQ7E5HGLQ5rEIttDF7u8cZ4pNiNMSPM7xmMbC-eK7S09hmsrN0EeXC7ZH38cw4ivywuoh4etzvCHfPn_a3d6V9w9fvt5u7kvDWzaVTDCGjRXWUFp3knEmDQWru9o0GqgFzjtJrZFaCNtwwE4Kw_u-aoFXsjHshrw79c2Gf82YJjW6ZHAYtMcwJ9UAg4ZTmYXyJDQxpBTRqkN0o45HRUEtRNVeXYiqheiSyURz6ZvzjLkbsb8UnhFmwduzQKeMz0btjUsXnayZrPni4eNJh5nIb4dRJePQG-xdRDOpPrj_cfPhnyZmcH5Z2xMeMe3DHH0mrqhKlQK1XS5gOQCogbaM_mB_AK1orgA</recordid><startdate>20070401</startdate><enddate>20070401</enddate><creator>Bernabeu, Eduardo, MD</creator><creator>Josa, Miguel, MD</creator><creator>Nomdedeu, Benet, MD, PhD</creator><creator>Ramírez, José, MD, PhD</creator><creator>García-Valentín, Antonio, MD</creator><creator>Mestres, Carlos A., MD, PhD</creator><creator>Mulet, Jaime, MD, PhD</creator><general>Elsevier Inc</general><general>Elsevier Science</general><scope>IQODW</scope><scope>CGR</scope><scope>CUY</scope><scope>CVF</scope><scope>ECM</scope><scope>EIF</scope><scope>NPM</scope><scope>AAYXX</scope><scope>CITATION</scope><scope>7X8</scope></search><sort><creationdate>20070401</creationdate><title>One-Step Surgical Approach of a Thoracic Aortic Aneurysm in Wiskott-Aldrich Syndrome</title><author>Bernabeu, Eduardo, MD ; Josa, Miguel, MD ; Nomdedeu, Benet, MD, PhD ; Ramírez, José, MD, PhD ; García-Valentín, Antonio, MD ; Mestres, Carlos A., MD, PhD ; Mulet, Jaime, MD, PhD</author></sort><facets><frbrtype>5</frbrtype><frbrgroupid>cdi_FETCH-LOGICAL-c493t-3533e7f5fc116b83438c10fab6c7a01f044b81fc8a55f740eb85c4dd2904287c3</frbrgroupid><rsrctype>articles</rsrctype><prefilter>articles</prefilter><language>eng</language><creationdate>2007</creationdate><topic>Adult</topic><topic>Angiography</topic><topic>Aortic Aneurysm, Thoracic - diagnostic imaging</topic><topic>Aortic Aneurysm, Thoracic - etiology</topic><topic>Aortic Aneurysm, Thoracic - surgery</topic><topic>Biological and medical sciences</topic><topic>Blood Vessel Prosthesis</topic><topic>Blood Vessel Prosthesis Implantation - methods</topic><topic>Brain Ischemia - prevention & control</topic><topic>Cardiopulmonary Bypass</topic><topic>Cardiothoracic Surgery</topic><topic>Follow-Up Studies</topic><topic>Hematologic and hematopoietic diseases</topic><topic>Humans</topic><topic>Immunodeficiencies</topic><topic>Immunodeficiencies. Immunoglobulinopathies</topic><topic>Immunopathology</topic><topic>Male</topic><topic>Medical sciences</topic><topic>Perfusion - methods</topic><topic>Platelet diseases and coagulopathies</topic><topic>Radiography, Thoracic</topic><topic>Risk Assessment</topic><topic>Severity of Illness Index</topic><topic>Surgery</topic><topic>Surgery (general aspects). Transplantations, organ and tissue grafts. Graft diseases</topic><topic>Surgery of the heart</topic><topic>Surgery of the respiratory system</topic><topic>Tomography, X-Ray Computed</topic><topic>Treatment Outcome</topic><topic>Wiskott-Aldrich Syndrome - complications</topic><topic>Wiskott-Aldrich Syndrome - diagnosis</topic><toplevel>peer_reviewed</toplevel><toplevel>online_resources</toplevel><creatorcontrib>Bernabeu, Eduardo, MD</creatorcontrib><creatorcontrib>Josa, Miguel, MD</creatorcontrib><creatorcontrib>Nomdedeu, Benet, MD, PhD</creatorcontrib><creatorcontrib>Ramírez, José, MD, PhD</creatorcontrib><creatorcontrib>García-Valentín, Antonio, MD</creatorcontrib><creatorcontrib>Mestres, Carlos A., MD, PhD</creatorcontrib><creatorcontrib>Mulet, Jaime, MD, PhD</creatorcontrib><collection>Pascal-Francis</collection><collection>Medline</collection><collection>MEDLINE</collection><collection>MEDLINE (Ovid)</collection><collection>MEDLINE</collection><collection>MEDLINE</collection><collection>PubMed</collection><collection>CrossRef</collection><collection>MEDLINE - Academic</collection><jtitle>The Annals of thoracic surgery</jtitle></facets><delivery><delcategory>Remote Search Resource</delcategory><fulltext>fulltext</fulltext></delivery><addata><au>Bernabeu, Eduardo, MD</au><au>Josa, Miguel, MD</au><au>Nomdedeu, Benet, MD, PhD</au><au>Ramírez, José, MD, PhD</au><au>García-Valentín, Antonio, MD</au><au>Mestres, Carlos A., MD, PhD</au><au>Mulet, Jaime, MD, PhD</au><format>journal</format><genre>article</genre><ristype>JOUR</ristype><atitle>One-Step Surgical Approach of a Thoracic Aortic Aneurysm in Wiskott-Aldrich Syndrome</atitle><jtitle>The Annals of thoracic surgery</jtitle><addtitle>Ann Thorac Surg</addtitle><date>2007-04-01</date><risdate>2007</risdate><volume>83</volume><issue>4</issue><spage>1537</spage><epage>1538</epage><pages>1537-1538</pages><issn>0003-4975</issn><eissn>1552-6259</eissn><coden>ATHSAK</coden><abstract>Wiskott-Aldrich syndrome is a primary immunodeficiency characterized by infections, thrombocytopenia, and eczema. We present a 33-year-old man with this syndrome who underwent a one-stage ascending aorta, aortic arch and descending aortic aneurysm repair under moderate hypothermia and continuous visceral and cerebral perfusion. Histologic examination showed the presence of an aortitis with granulomatous inflammatory response and multinucleated cells.</abstract><cop>New York, NY</cop><pub>Elsevier Inc</pub><pmid>17383380</pmid><doi>10.1016/j.athoracsur.2006.10.005</doi><tpages>2</tpages></addata></record> |
| fulltext | fulltext |
| identifier | ISSN: 0003-4975 |
| ispartof | The Annals of thoracic surgery, 2007-04, Vol.83 (4), p.1537-1538 |
| issn | 0003-4975 1552-6259 |
| language | eng |
| recordid | cdi_proquest_miscellaneous_70307418 |
| source | MEDLINE; Elektronische Zeitschriftenbibliothek - Frei zugängliche E-Journals; Alma/SFX Local Collection |
| subjects | Adult Angiography Aortic Aneurysm, Thoracic - diagnostic imaging Aortic Aneurysm, Thoracic - etiology Aortic Aneurysm, Thoracic - surgery Biological and medical sciences Blood Vessel Prosthesis Blood Vessel Prosthesis Implantation - methods Brain Ischemia - prevention & control Cardiopulmonary Bypass Cardiothoracic Surgery Follow-Up Studies Hematologic and hematopoietic diseases Humans Immunodeficiencies Immunodeficiencies. Immunoglobulinopathies Immunopathology Male Medical sciences Perfusion - methods Platelet diseases and coagulopathies Radiography, Thoracic Risk Assessment Severity of Illness Index Surgery Surgery (general aspects). Transplantations, organ and tissue grafts. Graft diseases Surgery of the heart Surgery of the respiratory system Tomography, X-Ray Computed Treatment Outcome Wiskott-Aldrich Syndrome - complications Wiskott-Aldrich Syndrome - diagnosis |
| title | One-Step Surgical Approach of a Thoracic Aortic Aneurysm in Wiskott-Aldrich Syndrome |
| url | https://sfx.bib-bvb.de/sfx_tum?ctx_ver=Z39.88-2004&ctx_enc=info:ofi/enc:UTF-8&ctx_tim=2025-02-05T12%3A45%3A27IST&url_ver=Z39.88-2004&url_ctx_fmt=infofi/fmt:kev:mtx:ctx&rfr_id=info:sid/primo.exlibrisgroup.com:primo3-Article-proquest_cross&rft_val_fmt=info:ofi/fmt:kev:mtx:journal&rft.genre=article&rft.atitle=One-Step%20Surgical%20Approach%20of%20a%20Thoracic%20Aortic%20Aneurysm%20in%20Wiskott-Aldrich%20Syndrome&rft.jtitle=The%20Annals%20of%20thoracic%20surgery&rft.au=Bernabeu,%20Eduardo,%20MD&rft.date=2007-04-01&rft.volume=83&rft.issue=4&rft.spage=1537&rft.epage=1538&rft.pages=1537-1538&rft.issn=0003-4975&rft.eissn=1552-6259&rft.coden=ATHSAK&rft_id=info:doi/10.1016/j.athoracsur.2006.10.005&rft_dat=%3Cproquest_cross%3E70307418%3C/proquest_cross%3E%3Curl%3E%3C/url%3E&disable_directlink=true&sfx.directlink=off&sfx.report_link=0&rft_id=info:oai/&rft_pqid=70307418&rft_id=info:pmid/17383380&rft_els_id=S000349750601931X&rfr_iscdi=true |