One-Step Surgical Approach of a Thoracic Aortic Aneurysm in Wiskott-Aldrich Syndrome

Wiskott-Aldrich syndrome is a primary immunodeficiency characterized by infections, thrombocytopenia, and eczema. We present a 33-year-old man with this syndrome who underwent a one-stage ascending aorta, aortic arch and descending aortic aneurysm repair under moderate hypothermia and continuous vis...

Ausführliche Beschreibung

Gespeichert in:

Bibliographische Detailangaben
Veröffentlicht in:	The Annals of thoracic surgery 2007-04, Vol.83 (4), p.1537-1538
Hauptverfasser:	Bernabeu, Eduardo, MD, Josa, Miguel, MD, Nomdedeu, Benet, MD, PhD, Ramírez, José, MD, PhD, García-Valentín, Antonio, MD, Mestres, Carlos A., MD, PhD, Mulet, Jaime, MD, PhD
Format:	Artikel
Sprache:	eng
Schlagworte:	Adult Angiography Aortic Aneurysm, Thoracic - diagnostic imaging Aortic Aneurysm, Thoracic - etiology Aortic Aneurysm, Thoracic - surgery Biological and medical sciences Blood Vessel Prosthesis Blood Vessel Prosthesis Implantation - methods Brain Ischemia - prevention & control Cardiopulmonary Bypass Cardiothoracic Surgery Follow-Up Studies Hematologic and hematopoietic diseases Humans Immunodeficiencies Immunodeficiencies. Immunoglobulinopathies Immunopathology Male Medical sciences Perfusion - methods Platelet diseases and coagulopathies Radiography, Thoracic Risk Assessment Severity of Illness Index Surgery Surgery (general aspects). Transplantations, organ and tissue grafts. Graft diseases Surgery of the heart Surgery of the respiratory system Tomography, X-Ray Computed Treatment Outcome Wiskott-Aldrich Syndrome - complications Wiskott-Aldrich Syndrome - diagnosis
Online-Zugang:	Volltext
Tags:	Tag hinzufügen Keine Tags, Fügen Sie den ersten Tag hinzu!

Beschreibung
Zusammenfassung:	Wiskott-Aldrich syndrome is a primary immunodeficiency characterized by infections, thrombocytopenia, and eczema. We present a 33-year-old man with this syndrome who underwent a one-stage ascending aorta, aortic arch and descending aortic aneurysm repair under moderate hypothermia and continuous visceral and cerebral perfusion. Histologic examination showed the presence of an aortitis with granulomatous inflammatory response and multinucleated cells.
ISSN:	0003-4975 1552-6259
DOI:	10.1016/j.athoracsur.2006.10.005