Intrathoracic malignant peripheral nerve sheath tumor with angiosarcoma in a child with NF1

Intrathoracic malignant peripheral nerve sheath tumor with angiosarcoma in a child with NF1

Malignant peripheral nerve sheath tumors (MPNSTs) are uncommon in children and adolescents but occur more frequently in NF1 patients. Angiosarcomatous differentiation in MPNSTs is a rare entity with poor prognosis. We report on a 13-year-old boy with intrathoracic angiosarcoma arising in MPNST assoc...

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Veröffentlicht in:Tumori 2007-11, Vol.93 (6), p.641-644
Hauptverfasser: Elli, Murat, Can, Bilge, Ceyhan, Meltem, Pinarli, Faruk Güçlü, Dagdemir, Ayhan, Ayyildiz, Halil Suat, Gürsel, Bilge, Dagçinar, Adnan
Format: Artikel
Sprache:eng
Schlagworte:
Adolescent
Hemangiosarcoma - pathology
Humans
Male
Neoplasms, Multiple Primary - pathology
Nerve Sheath Neoplasms - pathology
Neurofibromatosis 1 - pathology
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Zusammenfassung:Malignant peripheral nerve sheath tumors (MPNSTs) are uncommon in children and adolescents but occur more frequently in NF1 patients. Angiosarcomatous differentiation in MPNSTs is a rare entity with poor prognosis. We report on a 13-year-old boy with intrathoracic angiosarcoma arising in MPNST associated with NF1.
ISSN:0300-8916
2038-2529
DOI:10.1177/030089160709300625