Splenic infarction due to concomitant hereditary spherocytosis and sickle cell trait

Abstract Concomitant hereditary spherocytosis and sickle cell trait, although extremely rare, could potentially lead to splenic sequestration or infarction. We report here the first case of splenic infarction in a child with hereditary spherocytosis and sickle cell trait while flying on a commercial...

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Veröffentlicht in:	Journal of pediatric surgery 2007-12, Vol.42 (12), p.2129-2131
Hauptverfasser:	Dulman, Robin Yates, Buchanan, George R, Ginsburg, Howard, Fefferman, Nancy R, Greco, M. Alba, Borys, Dariusz, Blei, Francine
Format:	Artikel
Sprache:	eng
Schlagworte:	Biopsy, Needle Child Female Follow-Up Studies Humans Immunohistochemistry Pediatrics Risk Assessment Severity of Illness Index Sickle Cell Trait - complications Sickle Cell Trait - diagnosis Spherocytosis, Hereditary - complications Spherocytosis, Hereditary - diagnosis Splenectomy - methods Splenic Infarction - etiology Splenic Infarction - pathology Splenic Infarction - surgery Surgery Tomography, X-Ray Computed Treatment Outcome
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Zusammenfassung:	Abstract Concomitant hereditary spherocytosis and sickle cell trait, although extremely rare, could potentially lead to splenic sequestration or infarction. We report here the first case of splenic infarction in a child with hereditary spherocytosis and sickle cell trait while flying on a commercial aircraft. The presence of hypoxia, hemoconcentrated erythrocytes, and sickle hemoglobin created the perfect environment for clinical sequelae.
ISSN:	0022-3468 1531-5037
DOI:	10.1016/j.jpedsurg.2007.07.057