Ileal polyposis as manifestation of neurofibromatosis syndrome

A 13-year-old girl presented with features of intestinal obstruction. At surgery, the terminal 25 cm of ileum, which was resected along with the right colon, showed plexiform neurofibromatosis of the serosa and mesentery, hyperplastic submucosal and myenteric nerve plexuses and proliferation of neur...

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Veröffentlicht in:	Indian journal of gastroenterology 2006-05, Vol.25 (3), p.159-160
Hauptverfasser:	Sathe, Pragati A, Kulkarni, Varsha M, Raut, Abhijit A, Deolekar, Sameer S, Joshi, Amita S
Format:	Artikel
Sprache:	eng
Schlagworte:	Adolescent Cafe-au-Lait Spots - pathology Colectomy Colon - pathology Female Humans Ileum - pathology Intestinal Obstruction - etiology Intestinal Obstruction - pathology Intestinal Obstruction - surgery Intestinal Polyposis - etiology Intestinal Polyposis - pathology Intestinal Polyposis - surgery Laparotomy Neurofibromatoses - complications Neurofibromatoses - pathology Neurofibromatoses - surgery
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Beschreibung
Zusammenfassung:	A 13-year-old girl presented with features of intestinal obstruction. At surgery, the terminal 25 cm of ileum, which was resected along with the right colon, showed plexiform neurofibromatosis of the serosa and mesentery, hyperplastic submucosal and myenteric nerve plexuses and proliferation of neural tissue in the lamina propria, which manifested as diffuse polyposis of the ileal mucosa. The patient had a single inconspicuous external neurofibroma and a few café-au-lait spots on the back.
ISSN:	0254-8860