A case of systemic sclerosis complicated by idiopathic portal hypertension: case report and literature review

Abstract We encountered a 62-year-old woman who had systemic sclerosis (SSc) complicated by idiopathic portal hypertension (IPH). She had a 10-year history of scleroderma and Raynaud's phenomenon. She also had pancytopenia, splenomegaly, and esophageal varices. Treatment with prednisolone and e...

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Veröffentlicht in:	Modern rheumatology 2006-06, Vol.16 (3), p.183-187
Hauptverfasser:	Takagi, Kenji, Nishio, Shinichiro, Akimoto, Kimiko, Yoshino, Takumi, Kawai, Shinichi
Format:	Artikel
Sprache:	eng
Schlagworte:	Ascites - etiology Ascites - therapy Esophageal and Gastric Varices - etiology Esophageal and Gastric Varices - surgery Female Glucocorticoids - administration & dosage Humans Hypertension, Portal - complications Hypertension, Portal - etiology Ligation Middle Aged Pleural Effusion - etiology Pleural Effusion - therapy Prednisolone - administration & dosage Prognosis Raynaud Disease - complications Scleroderma, Systemic - complications
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Zusammenfassung:	Abstract We encountered a 62-year-old woman who had systemic sclerosis (SSc) complicated by idiopathic portal hypertension (IPH). She had a 10-year history of scleroderma and Raynaud's phenomenon. She also had pancytopenia, splenomegaly, and esophageal varices. Treatment with prednisolone and endoscopic variceal ligation resulted in improvement of her symptoms. According to our literature review, the prognosis of patients with SSc complicated by IPH is relatively poor. However, the factors that predict outcome of these patients have not been elucidated.
ISSN:	1439-7595 1439-7609
DOI:	10.3109/s10165-006-0479-1