Spontaneous Mesenteric Hemorrhage Associated With Ehlers-Danlos Syndrome

The vascular type of Ehlers-Danlos syndrome is a genetic disorder of connective tissue and is frequently associated with catastrophic arterial complications. Its surgical treatment is extremely difficult because of the fragility of vessels. This article describes three patients with vascular type of...

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Veröffentlicht in:	Journal of gastrointestinal surgery 2006-04, Vol.10 (4), p.583-585
Hauptverfasser:	Hosaka, Akihiro, Miyata, Tetsuro, Shigematsu, Hiroshi, Deguchi, Jun-o, Kimura, Hideo, Nagawa, Hirokazu, Sato, Osamu, Sakimoto, Takehiko, Mochizuki, Tomoyuki
Format:	Artikel
Sprache:	eng
Schlagworte:	Abdominal Cavity Adult Aneurysm - etiology Aneurysm, Dissecting - etiology Aortic Aneurysm, Abdominal - etiology Ehlers-Danlos syndrome Ehlers-Danlos Syndrome - complications Fatal Outcome Follow-Up Studies Hematoma - etiology Hemorrhage - etiology Hepatic Artery - pathology Humans Iliac Artery - pathology Jejunum - blood supply Male Mesenteric Arteries - pathology Mesenteric Artery, Inferior - pathology mesenteric hemorrhage Renal Artery - pathology Rupture, Spontaneous Splenic Artery - pathology surgical management
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Zusammenfassung:	The vascular type of Ehlers-Danlos syndrome is a genetic disorder of connective tissue and is frequently associated with catastrophic arterial complications. Its surgical treatment is extremely difficult because of the fragility of vessels. This article describes three patients with vascular type of Ehlers-Danlos syndrome who developed mesenteric hemorrhage due to spontaneous arterial rupture. The clinical and molecular characteristics of the disease are briefly reviewed.
ISSN:	1091-255X 1873-4626
DOI:	10.1016/j.gassur.2005.07.018