Chordoid Meningioma: The Rarest Subtype of Grade II Meningioma

Chordoid meningioma, a rare WHO grade II tumor, is known for its aggressive behavior and high recurrence rate. We report a case of a 44-year-old woman with progressive left-sided weakness, where imaging revealed a 3.0 cm lesion in the right sphenoidal wing with significant midline shift and edema. Following corticosteroid treatment, the patient underwent embolization and complete tumor resection, achieving full motor recovery. Pathology confirmed a chordoid meningioma. Gross total resection is vital to minimize the risk of recurrence, while subtotal resection is linked to higher recurrence, often with elevated MIB-1 scores. Adjuvant radiotherapy may be used in high-risk cases, though it carries a risk of malignant transformation. Early detection, complete resection, and close follow-up are key to optimal outcomes.