Glomangiopericytoma Presenting as a Middle Ear Mass

We describe an unusual case of glomangiopericytoma presenting as a mass filling the middle ear, enveloping the ossicles, and extending into the mastoid antrum without bony destruction. Management involved three surgeries and stereotactic radiosurgery, which achieved short‐term local control with no evidence of disease on MRI imaging 12 months after radiation. Facial nerve function and hearing were preserved. This is the first report to our knowledge of a glomangiopericytoma presenting as a primary temporal bone lesion. Treatment with surgery and stereotactic radiosurgery for residual or recurrent disease is a reasonable approach to achieve local control and functional preservation. Laryngoscope, 134:1426–1430, 2024 Glomangiopericytomas (GPCs) have rarely been reported to present outside the sinonasal cavity. We share our experience with managing a challenging, multiply recurrent GPC primary tumor in the middle ear with surgery and stereotactic radiosurgery. To our knowledge, this is the first description in the English language literature of GPC presenting as a temporal bone primary tumor.