Abnormal Left Ventricular Strain Correlates with Left Ventricular Dysfunction but not Aortic Pathology in Marfan Syndrome in Children

Abnormal Left Ventricular Strain Correlates with Left Ventricular Dysfunction but not Aortic Pathology in Marfan Syndrome in Children

Cardiomyopathy is a complication in adults with Marfan syndrome (MFS). Early recognition of MFS patients at high risk of cardiomyopathy could impact monitoring and treatment. Abnormal ventricular strain has been associated with impaired ventricular function among adults with MFS but remains understu...

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Veröffentlicht in:Pediatric cardiology 2023-10, Vol.44 (7), p.1536-1545
Hauptverfasser: Connell, Patrick S., Morris, Shaine A., Doan, Tam T., Weigand, Justin
Format: Artikel
Sprache:eng
Schlagworte:
Cardiac patients
Cardiac Surgery
Cardiology
Care and treatment
Marfan syndrome
Medicine
Medicine & Public Health
Vascular Surgery
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Zusammenfassung:Cardiomyopathy is a complication in adults with Marfan syndrome (MFS). Early recognition of MFS patients at high risk of cardiomyopathy could impact monitoring and treatment. Abnormal ventricular strain has been associated with impaired ventricular function among adults with MFS but remains understudied in children. We retrospectively analyzed a cohort of patients with MFS undergoing cardiac magnetic resonance imaging (CMR) performed in 2003–2018 at age 
ISSN:0172-0643
1432-1971
DOI:10.1007/s00246-023-03232-8