Congenital intra‐hepatic porto‐systemic shunts diagnosed during intrauterine life: Systematic review

Objective To describe the ultrasonographic characteristics of congenital porto‐systemic venous shunts (CPSS) diagnosed during pregnancy, their outcomes, and their evolution. Methods Two independent researchers selected 493 review articles and case reports through the analysis of titles, s, and full text. The PubMed and LILACS databases were searched. Through the application of filters according to the PRISMA protocol, only six articles were used in the research. The following information was collected, when available: gestational age at diagnosis, gender, birth weight, type of shunt, associated anomalies/complications and treatment/progression. Results The data were obtained from 27 cases, with 22 (82%) fetuses diagnosed with intra‐hepatic CPSS and 5 (18%) with extra‐hepatic CPSS. The median time of intrauterine diagnosis was 33 weeks. In 12 (57.1%) of the 21 pregnancies evaluated, delivery was preterm. The estimated fetal weight ranged from 1150 to 3760 g, with 4 (25%) cases at