Tracheobronchoplasty after a trial with a silicone Y-stent in a patient with Mounier-Kuhn syndrome
Abstract Tracheobronchomegaly or Mounier-Kuhn syndrome is a rare disorder characterized by the widening of the trachea and the main bronchi. It is a form of tracheomalacia called ‘cartilaginous malacic’ and is characterized by deformation of the tracheal cartilages and intrusion of the redundant mem...
Gespeichert in:
Veröffentlicht in: | European journal of cardio-thoracic surgery 2020-06, Vol.57 (6), p.1221-1223 |
---|---|
Hauptverfasser: | , , , |
Format: | Artikel |
Sprache: | eng |
Schlagworte: | |
Online-Zugang: | Volltext |
Tags: |
Tag hinzufügen
Keine Tags, Fügen Sie den ersten Tag hinzu!
|
Zusammenfassung: | Abstract
Tracheobronchomegaly or Mounier-Kuhn syndrome is a rare disorder characterized by the widening of the trachea and the main bronchi. It is a form of tracheomalacia called ‘cartilaginous malacic’ and is characterized by deformation of the tracheal cartilages and intrusion of the redundant membranous wall into the lumen of the airway. We present a patient with Mounier-Kuhn syndrome managed like patients with tracheomalacia of other aetiologies—a tracheobronchoplasty with a reconstructed D-shaped trachea and stabilization of the posterior membranous wall by attaching a polypropylene mesh to the posterior membranous wall of the trachea and the main bronchi after a trial period with a tracheobronchial Y-shaped silicone stent. |
---|---|
ISSN: | 1010-7940 1873-734X |
DOI: | 10.1093/ejcts/ezz317 |