Tracheobronchoplasty after a trial with a silicone Y-stent in a patient with Mounier-Kuhn syndrome

Abstract Tracheobronchomegaly or Mounier-Kuhn syndrome is a rare disorder characterized by the widening of the trachea and the main bronchi. It is a form of tracheomalacia called ‘cartilaginous malacic’ and is characterized by deformation of the tracheal cartilages and intrusion of the redundant mem...

Ausführliche Beschreibung

Gespeichert in:
Bibliographische Detailangaben
Veröffentlicht in:European journal of cardio-thoracic surgery 2020-06, Vol.57 (6), p.1221-1223
Hauptverfasser: Muñoz Fos, Anna, Cosano, Javier, Wins, Richard, Galán, Genaro
Format: Artikel
Sprache:eng
Schlagworte:
Online-Zugang:Volltext
Tags: Tag hinzufügen
Keine Tags, Fügen Sie den ersten Tag hinzu!
Beschreibung
Zusammenfassung:Abstract Tracheobronchomegaly or Mounier-Kuhn syndrome is a rare disorder characterized by the widening of the trachea and the main bronchi. It is a form of tracheomalacia called ‘cartilaginous malacic’ and is characterized by deformation of the tracheal cartilages and intrusion of the redundant membranous wall into the lumen of the airway. We present a patient with Mounier-Kuhn syndrome managed like patients with tracheomalacia of other aetiologies—a tracheobronchoplasty with a reconstructed D-shaped trachea and stabilization of the posterior membranous wall by attaching a polypropylene mesh to the posterior membranous wall of the trachea and the main bronchi after a trial period with a tracheobronchial Y-shaped silicone stent.
ISSN:1010-7940
1873-734X
DOI:10.1093/ejcts/ezz317