Surgical outcomes of cavovarus foot deformity in children with Charcot-Marie-Tooth disease

•First comprehensive study to investigate surgical outcomes in children with CMT.•Cavovarus surgery improved foot alignment, ankle flexibility, and daily trips/falls.•Plantar pressure loading improved beneath the rearfoot and lateral midfoot.•Strength, function and quality of life generally mirrored...

Ausführliche Beschreibung

Gespeichert in:
Bibliographische Detailangaben
Veröffentlicht in:Neuromuscular disorders : NMD 2019-06, Vol.29 (6), p.427-436
Hauptverfasser: Lin, Ting, Gibbons, Paul, Mudge, Anita J., Cornett, Kayla M.D., Menezes, Manoj P., Burns, Joshua
Format: Artikel
Sprache:eng
Schlagworte:
Online-Zugang:Volltext
Tags: Tag hinzufügen
Keine Tags, Fügen Sie den ersten Tag hinzu!
Beschreibung
Zusammenfassung:•First comprehensive study to investigate surgical outcomes in children with CMT.•Cavovarus surgery improved foot alignment, ankle flexibility, and daily trips/falls.•Plantar pressure loading improved beneath the rearfoot and lateral midfoot.•Strength, function and quality of life generally mirrored the natural course of CMT. Charcot-Marie-Tooth disease (CMT) causes disabling cavovarus foot deformity. Orthopaedic surgery is performed in severe cases; however few studies have investigated whether surgery improves health outcomes during childhood. This study investigated the impact of cavovarus surgery on validated physical, functional, parent/self-reported and biomechanical measures in 21 consecutive patients (mean age at surgery 12.5 years, SD 2.7) evaluated before and after surgery (mean duration 15.7 months, SD 5.9), and compared to natural history data from 206 children with CMT. Measures from the CMT Pediatric Scale evaluated foot alignment (Foot Posture Index), ankle flexibility (lunge test), strength (foot dorsiflexion/plantarflexion by hand-held dynamometry), function (balance, long jump, 6-minute walk test) and self-reported symptoms. Quality of life (Child Health Questionnaire) and gait (pressure loading) were also assessed. Foot Posture Index and lunge improved with surgery by 6.0 points (SD 3.2) and 6.1° (SD 7.3) respectively (p
ISSN:0960-8966
1873-2364
DOI:10.1016/j.nmd.2019.04.004