Complete repair with unifocalization of the only unilateral lung

Complete repair with unifocalization of the only unilateral lung

A boy with 22q11.2 deletion was diagnosed with pulmonary atresia with ventricular septal defect (PAVSD) and major aortopulmonary collateral arteries (MAPCAs). At 8 months, unifocalization of left MAPCAs and BT shunt was performed at another hospital. However, they occluded directly after surgery. An...

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Veröffentlicht in:General thoracic and cardiovascular surgery 2020-05, Vol.68 (5), p.538-541
Hauptverfasser: Ishidou, Motonori, Ota, Keisuke, Kanno, Kazuyoshi, Murata, Masaya, Hirose, Keiichi, Nagato, Hisao, Sakamoto, Kisaburo, Ikai, Akio
Format: Artikel
Sprache:eng
Schlagworte:
Cardiac Surgery
Cardiology
Case Report
Lungs
Medical imaging
Medicine
Medicine & Public Health
Ostomy
Oxygen saturation
Patients
Physiology
Pulmonary arteries
Scintigraphy
Surgery
Surgical Oncology
Surgical outcomes
Thoracic Surgery
Tomography
Veins & arteries
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Zusammenfassung:A boy with 22q11.2 deletion was diagnosed with pulmonary atresia with ventricular septal defect (PAVSD) and major aortopulmonary collateral arteries (MAPCAs). At 8 months, unifocalization of left MAPCAs and BT shunt was performed at another hospital. However, they occluded directly after surgery. An angiography revealed 2 MAPCAs supplying all segments of the right lung. Qp:Qs was 2.24. At 1 year 6 months, we performed VSD closure with unifocalization of the only right lung vascularity, using intraoperative PA flow study. We report a successful case of complete repair with unilateral lung in PAVSD and MAPCAs.
ISSN:1863-6705
1863-6713
DOI:10.1007/s11748-019-01109-3