Segmental Hailey‐Hailey disease of the vulva

Segmental Hailey‐Hailey disease of the vulva

A female infant presented with an ulcerated lesion on the right side of the vulva. Histopathology showed a suprabasal acantholytic blister with intact papillae protruding into the blister cavity and a few dyskeratotic cells. There were no signs of injury on other locations. Family history was unrema...

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Veröffentlicht in:Pediatric dermatology 2018-11, Vol.35 (6), p.e398-e399
Hauptverfasser: García‐Morales, Irene, Requena‐Caballero, Luis, Happle, Rudolf, Torrelo, Antonio
Format: Artikel
Sprache:eng
Schlagworte:
Acantholysis - pathology
Autoimmune diseases
Babies
Female
Hailey‐Hailey disease
Humans
Infant
Medical diagnosis
Mosaicism
Papillae
Pemphigus, Benign Familial - diagnosis
Skin diseases
Vulva
Vulva - pathology
Vulvar Diseases - pathology
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Beschreibung
Zusammenfassung:A female infant presented with an ulcerated lesion on the right side of the vulva. Histopathology showed a suprabasal acantholytic blister with intact papillae protruding into the blister cavity and a few dyskeratotic cells. There were no signs of injury on other locations. Family history was unremarkable. Our patient may have linear Hailey‐Hailey disease of the vulva, most likely a case of type 1 mosaic.
ISSN:0736-8046
1525-1470
DOI:10.1111/pde.13625