Treatment of mediastinal lymphatic malformation in children: an analysis of a nationwide survey in Japan

Purpose Clinical guidelines on lymphatic malformation (LM) influencing the airway have been crafted in the Research Project for Intractable Diseases. We herein report an analysis of a nationwide survey of mediastinal LM and the therapeutic recommendations. Methods Eighty-seven registered cases with mediastinal involvement were analyzed with a review of the literature. Results Mediastinal LM was located more often in the upper and anterior mediastinum and was found without any accompanying symptoms in 56/87 cases. Tracheostomy was required in 23/87 cases, mostly