Left Ventricular Function In Children And Adolescents With Arrhythmogenic Right Ventricular Cardiomyopathy

Abstract The aim of this study was to determine if left ventricular (LV) contractility is reduced in children with arrhythmogenic right ventricular cardiomyopathy (ARVC). For this retrospective study, children and adolescents undergoing a work-up for ARVC were characterized according to the revised Task Force Criteria (rTFC). LV strain, rotation, and torsion were measured by feature tracking CMR. Of 142 pediatric patients 41% had no, 23% possible, 20% borderline and 16% definite ARVC. LV ejection fraction (EF) did not differ between rTFC categories. Patients in higher rTFC categories had lower right ventricular (RV) EF z scores (Z-), higher Z-RV end diastolic volume (EDVs) and larger Z-LVEDVs (p