Gastrointestinal Erdheim-Chester disease
We report a rare case of Erdheim-Chester Disease, a non-Langerhans cell histiocytosis. A 60-year old female presented with a seven-month history of vague abdominal symptoms. A large retroperitoneal mass was detected on computed tomography (CT), but multiple CT-guided biopsy samples were inconclusive...
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Veröffentlicht in: | Irish medical journal 2014-05, Vol.107 (5), p.149-150 |
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creator | Tevlin, R Cahalane, A M Larkin, J O Treacy, A Connaghan, D Winter, D C |
description | We report a rare case of Erdheim-Chester Disease, a non-Langerhans cell histiocytosis. A 60-year old female presented with a seven-month history of vague abdominal symptoms. A large retroperitoneal mass was detected on computed tomography (CT), but multiple CT-guided biopsy samples were inconclusive. Laparoscopy revealed a mass in the distal ileum, which was resected. Histology and immuno-histochemistry supported a diagnosis of Erdheim-Chester Disease. |
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A 60-year old female presented with a seven-month history of vague abdominal symptoms. A large retroperitoneal mass was detected on computed tomography (CT), but multiple CT-guided biopsy samples were inconclusive. Laparoscopy revealed a mass in the distal ileum, which was resected. 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A 60-year old female presented with a seven-month history of vague abdominal symptoms. A large retroperitoneal mass was detected on computed tomography (CT), but multiple CT-guided biopsy samples were inconclusive. Laparoscopy revealed a mass in the distal ileum, which was resected. Histology and immuno-histochemistry supported a diagnosis of Erdheim-Chester Disease.</description><subject>Diagnosis, Differential</subject><subject>Erdheim-Chester Disease - diagnosis</subject><subject>Erdheim-Chester Disease - surgery</subject><subject>Female</subject><subject>Humans</subject><subject>Ileum - pathology</subject><subject>Ileum - surgery</subject><subject>Middle Aged</subject><subject>Rare Diseases</subject><subject>Treatment Outcome</subject><issn>0332-3102</issn><fulltext>true</fulltext><rsrctype>article</rsrctype><creationdate>2014</creationdate><recordtype>article</recordtype><sourceid>EIF</sourceid><recordid>eNo1j01LxDAURbNQnHH0L8gsZ1NI3kvTdCllHIUBN7ouL80rE-mXSbvw31twXF24HA733oitRIQMlYSNuE_pS0oELOBObECX0lqjtuJwojTHMQwzpzkM1O2P0V849Fl1WRuOex8SU-IHcdtSl_jxmjvx-XL8qF6z8_vprXo-Z5MCM2e20ExUFr5Fkg69tl41JbIyaC25FksnrWu0B69yQ2DZlx4aVGRybMDiThz-vFMcv5d1Qt2H1HDX0cDjkmqVo9bGWIAVfbqii-vZ11MMPcWf-v8d_gLSm0mg</recordid><startdate>201405</startdate><enddate>201405</enddate><creator>Tevlin, R</creator><creator>Cahalane, A M</creator><creator>Larkin, J O</creator><creator>Treacy, A</creator><creator>Connaghan, D</creator><creator>Winter, D C</creator><scope>CGR</scope><scope>CUY</scope><scope>CVF</scope><scope>ECM</scope><scope>EIF</scope><scope>NPM</scope><scope>7X8</scope></search><sort><creationdate>201405</creationdate><title>Gastrointestinal Erdheim-Chester disease</title><author>Tevlin, R ; Cahalane, A M ; Larkin, J O ; Treacy, A ; Connaghan, D ; Winter, D C</author></sort><facets><frbrtype>5</frbrtype><frbrgroupid>cdi_FETCH-LOGICAL-p126t-874eaa97df3a0b3d48d1c93e16388abf39b08bc4d2d156a28ed9d2c31a653c283</frbrgroupid><rsrctype>articles</rsrctype><prefilter>articles</prefilter><language>eng</language><creationdate>2014</creationdate><topic>Diagnosis, Differential</topic><topic>Erdheim-Chester Disease - diagnosis</topic><topic>Erdheim-Chester Disease - surgery</topic><topic>Female</topic><topic>Humans</topic><topic>Ileum - pathology</topic><topic>Ileum - surgery</topic><topic>Middle Aged</topic><topic>Rare Diseases</topic><topic>Treatment Outcome</topic><toplevel>peer_reviewed</toplevel><toplevel>online_resources</toplevel><creatorcontrib>Tevlin, R</creatorcontrib><creatorcontrib>Cahalane, A M</creatorcontrib><creatorcontrib>Larkin, J O</creatorcontrib><creatorcontrib>Treacy, A</creatorcontrib><creatorcontrib>Connaghan, D</creatorcontrib><creatorcontrib>Winter, D C</creatorcontrib><collection>Medline</collection><collection>MEDLINE</collection><collection>MEDLINE (Ovid)</collection><collection>MEDLINE</collection><collection>MEDLINE</collection><collection>PubMed</collection><collection>MEDLINE - Academic</collection><jtitle>Irish medical journal</jtitle></facets><delivery><delcategory>Remote Search Resource</delcategory><fulltext>fulltext</fulltext></delivery><addata><au>Tevlin, R</au><au>Cahalane, A M</au><au>Larkin, J O</au><au>Treacy, A</au><au>Connaghan, D</au><au>Winter, D C</au><format>journal</format><genre>article</genre><ristype>JOUR</ristype><atitle>Gastrointestinal Erdheim-Chester disease</atitle><jtitle>Irish medical journal</jtitle><addtitle>Ir Med J</addtitle><date>2014-05</date><risdate>2014</risdate><volume>107</volume><issue>5</issue><spage>149</spage><epage>150</epage><pages>149-150</pages><issn>0332-3102</issn><abstract>We report a rare case of Erdheim-Chester Disease, a non-Langerhans cell histiocytosis. A 60-year old female presented with a seven-month history of vague abdominal symptoms. A large retroperitoneal mass was detected on computed tomography (CT), but multiple CT-guided biopsy samples were inconclusive. Laparoscopy revealed a mass in the distal ileum, which was resected. Histology and immuno-histochemistry supported a diagnosis of Erdheim-Chester Disease.</abstract><cop>Ireland</cop><pmid>24908861</pmid><tpages>2</tpages></addata></record> |
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subjects | Diagnosis, Differential Erdheim-Chester Disease - diagnosis Erdheim-Chester Disease - surgery Female Humans Ileum - pathology Ileum - surgery Middle Aged Rare Diseases Treatment Outcome |
title | Gastrointestinal Erdheim-Chester disease |
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