Gastrointestinal Erdheim-Chester disease

Gastrointestinal Erdheim-Chester disease

We report a rare case of Erdheim-Chester Disease, a non-Langerhans cell histiocytosis. A 60-year old female presented with a seven-month history of vague abdominal symptoms. A large retroperitoneal mass was detected on computed tomography (CT), but multiple CT-guided biopsy samples were inconclusive...

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Veröffentlicht in:Irish medical journal 2014-05, Vol.107 (5), p.149-150
Hauptverfasser: Tevlin, R, Cahalane, A M, Larkin, J O, Treacy, A, Connaghan, D, Winter, D C
Format: Artikel
Sprache:eng
Schlagworte:
Diagnosis, Differential
Erdheim-Chester Disease - diagnosis
Erdheim-Chester Disease - surgery
Female
Humans
Ileum - pathology
Ileum - surgery
Middle Aged
Rare Diseases
Treatment Outcome
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Beschreibung
Zusammenfassung:We report a rare case of Erdheim-Chester Disease, a non-Langerhans cell histiocytosis. A 60-year old female presented with a seven-month history of vague abdominal symptoms. A large retroperitoneal mass was detected on computed tomography (CT), but multiple CT-guided biopsy samples were inconclusive. Laparoscopy revealed a mass in the distal ileum, which was resected. Histology and immuno-histochemistry supported a diagnosis of Erdheim-Chester Disease.
ISSN:0332-3102