Recurrent Thymoma With Stiff-Person Syndrome and Pure Red Blood Cell Aplasia
Stiff-person syndrome (formerly known as stiff-man syndrome) is a very rare autoimmune and neurogenic disorder, thought to present as a paraneoplastic variant in association with thymoma. Pure red blood cell aplasia is also a paraneoplastic disorder associated with thymoma. Although separate cases o...
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Veröffentlicht in: | The Annals of thoracic surgery 2014-05, Vol.97 (5), p.1802-1804 |
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Format: | Artikel |
Sprache: | eng |
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Zusammenfassung: | Stiff-person syndrome (formerly known as stiff-man syndrome) is a very rare autoimmune and neurogenic disorder, thought to present as a paraneoplastic variant in association with thymoma. Pure red blood cell aplasia is also a paraneoplastic disorder associated with thymoma. Although separate cases of stiff-person syndrome and pure red blood cell aplasia have been reported, we describe here what is to our knowledge the first case of recurrent thymoma with both stiff-person syndrome and pure red blood cell aplasia. We describe the successful treatment of the neurogenic symptoms of stiff-person syndrome and the progressive anemia associated with pure red blood cell aplasia by tumor excision. |
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ISSN: | 0003-4975 1552-6259 |
DOI: | 10.1016/j.athoracsur.2013.07.103 |