A single-institution retrospective cases series of childhood undifferentiated embryonal liver sarcoma (UELS): success of combined therapy and the use of orthotopic liver transplant

A single-institution retrospective cases series of childhood undifferentiated embryonal liver sarcoma (UELS): success of combined therapy and the use of orthotopic liver transplant

Undifferentiated embryonal liver sarcoma (UELS) makes up 9% to 15% of all malignant liver tumors in children. UELS is characteristically diagnosed between the ages of 6 and 10 years and presents with abdominal pain, vomiting, and an abdominal mass. There is currently no standardized treatment for UE...

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Veröffentlicht in:Journal of pediatric hematology/oncology 2013-08, Vol.35 (6), p.451-455
Hauptverfasser: Plant, Ashley S, Busuttil, Ronald W, Rana, Abbas, Nelson, Scott D, Auerbach, Martin, Federman, Noah C
Format: Artikel
Sprache:eng
Schlagworte:
Adolescent
Antineoplastic Agents - therapeutic use
Child
Combined Modality Therapy
Female
Humans
Liver Neoplasms - diagnostic imaging
Liver Neoplasms - mortality
Liver Neoplasms - therapy
Liver Transplantation
Male
Multimodal Imaging
Positron-Emission Tomography
Radiotherapy
Retrospective Studies
Sarcoma - diagnostic imaging
Sarcoma - mortality
Sarcoma - therapy
Tomography, X-Ray Computed
Young Adult
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Zusammenfassung:Undifferentiated embryonal liver sarcoma (UELS) makes up 9% to 15% of all malignant liver tumors in children. UELS is characteristically diagnosed between the ages of 6 and 10 years and presents with abdominal pain, vomiting, and an abdominal mass. There is currently no standardized treatment for UELS except attempt at complete surgical resection. There have been only about 150 cases of UELS reported in the literature all with historically poor overall survival of
ISSN:1077-4114
1536-3678
DOI:10.1097/MPH.0b013e318271c948