From Silence to Sound - A Case of Autoimmune Ear Disease Mahabaleshwar Mamadapur,Varuni Pragya, Neethu

Abstract Autoimmune inner ear disease (AIED) is a rare rheumatological cause of sensorineural hearing loss, accounting for less than 1% of worldwide hearing loss. [...]AIED is a challenging diagnosis based on exclusion. Keywords Autoimmune, Sensorineural hearing loss, Autoimmune Ear Disease, Progressive Hearing Loss Introduction Autoimmune inner ear disease (AIED) is a rare rheumatological cause of sensorineural hearing loss, which accounts for less than 1% of hearing loss worldwide. [...]AIED is a challenging diagnosis based on exclusion121. The pace of hearing loss is too rapid to align with a presbycusis diagnosis and too gradual to characterize SNHL definitively/71 Hearing loss can result from the abnormal cochlea, auditory nerve function, or higher central auditory perception or processing aspects. Conclusion Autoimmune inner ear disease (AIED) is a rare rheumatological sensorineural hearing loss which accounts for less than 1% of hearing loss worldwide.