Enterocutaneous fistula in a hemophilia B patient: case report

Background: Hemophilia B is a rare entity than other coagulation disorders. It is an X-linked disorder characterized by a deficiency of functionally active coagulation factor IX (FIX), resulting in spontaneous or trauma-induced bleeding primarily in joints, muscles, and soft tissues. Case Presentati...

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Veröffentlicht in:European Journal of Medical Case Reports 2020, Vol.4 (11), p.384-386
Hauptverfasser: Shahid, Sana, Khan, Hina Abdul Qayoom, Saeed, Summaya, Agha, Jan Muhammad, Samo, Khursheed A., Abbasi, Mujeeb ur Rehman, Memon, Amjad Siraj
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Sprache:eng
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Zusammenfassung:Background: Hemophilia B is a rare entity than other coagulation disorders. It is an X-linked disorder characterized by a deficiency of functionally active coagulation factor IX (FIX), resulting in spontaneous or trauma-induced bleeding primarily in joints, muscles, and soft tissues. Case Presentation: We report a case of a female who presented with a surgical problem. She had a history of massive transfusion many years back. She bled perioperatively and then we investigated her and luckily found the deficiency of FIX. She was managed and discharged home well. Conclusion: Surgeons rarely comes across this rare coagulation disorder, so this was an intriguing case in view of the unusual presentation, initial diagnostic dilemma, and challenges in management.
ISSN:2520-4998
2520-4998
DOI:10.24911/ejmcr/173-1589881846