AIP, Jo-1 and ECMO

CT scan of the chest showed features consistent with ARDS (Acute Respiratory Distress Syndrome) (figure 1B). There are reports of the successful use of all these therapies in ASSD-ILD,2–7 although the evidence is generally limited to case series. [...]we have had some success using these drugs, in other patients with less severe ASSD-ILD. Screening for ANA, anti Cyclic citrullinated peptides (anti-CCP) and autoantibodies, including antisynthetase and myositis-associated antibodies, in all patients presenting with unexplained severe respiratory failure recalcitrant to initial therapy may help in diagnosis, as peripheral clinical signs of systemic rheumatic diseases can be very subtle. S9 Acute inflammatory presentation associates with survival in interstitial lung disease and extracorporeal membrane oxygenation-requiring severe respiratory failure: a single centre case series.