Alveolar rhabdomyosarcoma presenting as a lung mass: an uncommon presentation of a less common tumor

According to the TNM Classification of malignant tumours (TNM), it was categorised as stage III, T2b N0 M0. The case was discussed with thoracic surgeons from two other tertiary centres who decided to defer surgery since the interval MRI abdomen showed a reduction in the tumour size ( figure 7 ). [...]a decision was made to start radiation therapy (XRT) and continue chemotherapy. The alveolar subtype (ARMS) constitutes approximately another 20% of RMS cases. 2 ARMSs differ from embryonal RMS by its occurrence in older patients, distinctive pseudo alveolar pattern, the general absence of strap cells and strong myogenin rather than MyoD1 expression. 3 Multimodality treatment protocols, including surgery, radiotherapy and combination chemotherapy with vincristine, adriamycin and cyclophosphamide, have improved the outcome in the past decades.