Outcome of patients with NEMO deficiency following allogeneic hematopoietic cell transplant

Capsule Summary Patients with NEMO deficiency tolerate myeloablative hematopoietic stem cell conditioning and transplant, and most patients achieve adequate immune reconstitution to correct the underlying immune deficiency.

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Bibliographische Detailangaben
Veröffentlicht in:	Journal of allergy and clinical immunology 2017-03, Vol.139 (3), p.1040-1043.e2
Hauptverfasser:	Chandrakasan, Shanmuganathan, MD, Marsh, Rebecca A., MD, Uzel, Gulbu, MD, Holland, Steven M., MD, Shah, Kara N., MD, PhD, Bleesing, Jack, MD, PhD
Format:	Artikel
Sprache:	eng
Schlagworte:	Adenoviruses Adolescent Allergy and Immunology Allografts Bacterial infections Bone marrow Child Child, Preschool Defects Ectodermal Dysplasia - etiology Ectodermal Dysplasia - therapy Hematopoietic Stem Cell Transplantation - methods Herpes viruses Humans I-kappa B Kinase - deficiency Immunoglobulins Immunologic Deficiency Syndromes - etiology Immunologic Deficiency Syndromes - therapy Infections Inflammatory bowel disease Male Mutation Neutrophils Patients Stem cells Tetanus Treatment Outcome Viral infections
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Beschreibung
Zusammenfassung:	Capsule Summary Patients with NEMO deficiency tolerate myeloablative hematopoietic stem cell conditioning and transplant, and most patients achieve adequate immune reconstitution to correct the underlying immune deficiency.
ISSN:	0091-6749 1097-6825
DOI:	10.1016/j.jaci.2016.08.039