PREVALENCE AND CORRELATES OF LEFT VENTRICULAR CONTRACTILE DYSFUNCTION IN FABRY DISEASE

 Global Longitudinal Systolic Strain, %  Echocardiographic Parameter 1st Tertile (Range -23.7, -18.0) 2nd Tertile (Range -17.9, -15.2) 3rd Tertile (Range -14.9, -4.2) P value LV wall thickness, cm 2.49±0.66 2.63±0.54 3.04±0.75 0.004 Relative wall thickness 0.60±0.20 0.59±0.15 0.71±0.23 0.047...

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Veröffentlicht in:Journal of the American College of Cardiology 2012-03, Vol.59 (13), p.E1297-E1297
Hauptverfasser: Uraizee, Imran, Cheng, Susan, Wu, Justina, Shah, Beejal, O'Brien, Kaitlyn, Skali, Hicham, Solomon, Scott
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Sprache:eng
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Zusammenfassung: Global Longitudinal Systolic Strain, %  Echocardiographic Parameter 1st Tertile (Range -23.7, -18.0) 2nd Tertile (Range -17.9, -15.2) 3rd Tertile (Range -14.9, -4.2) P value LV wall thickness, cm 2.49±0.66 2.63±0.54 3.04±0.75 0.004 Relative wall thickness 0.60±0.20 0.59±0.15 0.71±0.23 0.047 LV mass, g 228.5±89.0 276.0±95.4 340.0±170.1 0.001 LV mass index, g/m2 129.8±43.4 147.1±57.1 179.9±78.1 0.006 LV end-diastolic diameter, cm 4.21±0.49 4.51±0.51 4.38±0.67 0.15 LV end-diastolic volume, mL 83.1±14.6 95.3±23.1 96.5±31.1 0.046 LV ejection fraction, % 69.9±6.3 65.4±7.3 66.0±6.2 0.028 Global longitudinal strain, % -20.1±1.7 -16.6±0.9 -12.3±2.4
ISSN:0735-1097
1558-3597
DOI:10.1016/S0735-1097(12)61298-4